Abstract
Plastic bronchitis is a rare condition characterized by the formation and expectoration of long, branching bronchial casts that develop in the tracheobronchial tree and cause airway obstruction. Plastic bronchitis has become increasingly recognized as a feared complication of the Fontan operation with a mortality of up to 50%. We report an 11 year old boy who developed severe plastic bronchitis following Fontan repair and the successful long-term control of cast formation utilizing a low-fat diet and subsequent thoracic duct ligation.
Original language | English (US) |
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Pages (from-to) | 47-52 |
Number of pages | 6 |
Journal | Lymphology |
Volume | 45 |
Issue number | 2 |
State | Published - Jun 2012 |
Keywords
- Chyloptysis
- Fontan procedure
- Low fat diet
- Lymphscintigram
- Plastic bronchitis
- Thoracic- duct ligation
ASJC Scopus subject areas
- Immunology and Allergy
- Hematology