Lymphangioleiomyomatosis and SZ α1-antitrypsin disease: A unique combination?

Andrew L. Chan, Sunye Kwack, Kirk D. Jones, Marilyn K. Glassberg, Charles R. Gherman

Research output: Contribution to journalArticlepeer-review

6 Scopus citations


We deseribe a case of a 37-year-old female ex-smoker with lymphangioleiomyomatosis and SZ α1-antitrypsin disease who underwent successful bilateral sequential lung transplantation. While this disease combination has not been described previously, we recommend vigilance for the possibility of sueh combinations in patients with chronic lung disease. The possible mechanisms of interaction resulting from both disease processes are discussed.

Original languageEnglish (US)
Pages (from-to)763-765
Number of pages3
Issue number2
StatePublished - Aug 1 2003
Externally publishedYes


  • COPD
  • Chylothorax
  • Lymphangioleiomyomatosis
  • Matrix metalloproteinase
  • SZ α-antitrypsin disease

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine
  • Critical Care and Intensive Care Medicine
  • Cardiology and Cardiovascular Medicine


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