IMAGING OF LYMPHATIC DYSPLASIA IN NOONAN SYNDROME: CASE STUDIES AND HISTORICAL ATLAS

T. Cox; C. Vance; S. Daley; C. Papendieck; H. McGregor; P. H. Kuo; Marlys H. Witte

doi:10.2458/LYMPH.4679

IMAGING OF LYMPHATIC DYSPLASIA IN NOONAN SYNDROME: CASE STUDIES AND HISTORICAL ATLAS

T. Cox, C. Vance, S. Daley, C. Papendieck, H. McGregor, P. H. Kuo, Marlys H. Witte

Research output: Contribution to journal › Article › peer-review

3 Scopus citations

Abstract

To determine the historical use and utility of various lymphatic imaging modalities in Noonan syndrome (NS) patients, we performed a comprehensive literature review by collecting the published medical imaging of NS lymphatic dysplasias. We correlated imaging findings with clinical phenotypes and treatment. Our analysis of lymphatic imaging modalities provides an algorithmic approach to imaging and patient care across the spectrum of NS developmental defects. A total of 54 NS cases have been published since 1975. Using the observations reported in 15 reviewed publications, an association was made between disruptions in central lymphatic flow and poor clinical presentations/outcomes in NS patients.

Original language	English (US)
Pages (from-to)	23-40
Number of pages	18
Journal	Lymphology
Volume	54
Issue number	1
DOIs	https://doi.org/10.2458/LYMPH.4679
State	Published - 2021

Keywords

Algorithm
Atlas
Imaging
Lymphangiography
Lymphatic imaging
Lymphatic vessel dysplasia
Noonan syndrome
Thoracic duct

ASJC Scopus subject areas

Immunology and Allergy
Hematology

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10.2458/LYMPH.4679

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abstract = "To determine the historical use and utility of various lymphatic imaging modalities in Noonan syndrome (NS) patients, we performed a comprehensive literature review by collecting the published medical imaging of NS lymphatic dysplasias. We correlated imaging findings with clinical phenotypes and treatment. Our analysis of lymphatic imaging modalities provides an algorithmic approach to imaging and patient care across the spectrum of NS developmental defects. A total of 54 NS cases have been published since 1975. Using the observations reported in 15 reviewed publications, an association was made between disruptions in central lymphatic flow and poor clinical presentations/outcomes in NS patients.",

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IMAGING OF LYMPHATIC DYSPLASIA IN NOONAN SYNDROME: CASE STUDIES AND HISTORICAL ATLAS

Abstract

Keywords

ASJC Scopus subject areas

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