Abstract
In their 1982 paper, Frank Marcus from the University of Arizona and Guy Fontaine with the group of investigators from the Hôpital de La Salpêtrière provided a detailed description of the disease they called "arrhythmogenic right ventricular dysplasia," or ARVD. They defined ARVD as a disorder of a heart muscle, leading to arrhythmias, and predominantly involving the right ventricular (RV) myocardium, causing progressive fibro fatty replacement of the RV free wall and subsequent RV enlargement and focal regional wall motion abnormalities. The authors described in detail imaging-based features of this disorder; utilizing RV angiography and echocardiography. They revealed the most frequent an involvement of specific regions of the RV (RV inflow tract and outflow tract and RV apex) defining it as "the triangle of dysplasia." In this Chapter, we provide historical overview of the changes in understanding and definition of ARVC/D. We also describe diagnostic approach utilizing the 2010 ARVC/D Task Force Criteria.
Original language | English (US) |
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Title of host publication | Cardiac MRI in the Diagnosis, Clinical Management, and Prognosis of Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia |
Publisher | Elsevier Inc. |
Pages | 35-51 |
Number of pages | 17 |
ISBN (Print) | 9780128012833 |
DOIs | |
State | Published - Mar 10 2016 |
Keywords
- ARVC/D
- Clinical diagnosis
- Definition
- Task Force Criteria
ASJC Scopus subject areas
- General Medicine
- General Social Sciences